Budd-Chiari Syndrome: An Unusual Complication of AL amyloidosis
نویسندگان
چکیده
منابع مشابه
Budd-Chiari Syndrome: An Unusual Presentation of Multisystemic Sarcoidosis
Sarcoidosis is a multisystem granulomatous disease of unknown origin. All organs may be affected. Liver involvement is common but it is rarely symptomatic. Only a few cases of Budd-Chiari syndrome (BCS) secondary to a hepatic sarcoidosis have been described so far. We describe a case of multisystemic sarcoidosis presenting with BCS. A 42-year old female was referred to our department for chroni...
متن کاملBudd Chiari syndrome: a rare complication of renal cancer.
A 52 years old lady was admitted with 2 weeks history of abdominal distension and drowsiness. Laboratory workup confirmed the presence of de-compensated liver disease with negative viral serology. Abdominal ultrasound and CT abdomen revealed tumour in right kidney with tumour thrombus extending in inferior vena cava and hepatic vein resulting in Budd Chiari syndrome and ascites. Patient was man...
متن کاملBudd-Chiari Syndrome
Budd-Chiari syndrome (BCS) is a rare condition which occurs when there is obstruction of the hepatic veins. It includes any condition in which there is obstruction to venous flow from the small hepatic veins to the inferior vena cava. It should be differentiated from veno-occlusive disease in which the sinusoidal epithelial cells of the hepatic venules are damaged; this mainly occurs after stem...
متن کاملBudd-Chiari syndrome.
Budd-Chiari syndrome is the generic term for different forms of hepatic venous outflow obstruction resulting in a clinical picture of portal hypertension and hepatomegaly. Three levels of venous outflow obstruction may be recognized, affecting respectively the small intrahepatic (IVC). Each level of obstruction is related to a different aetiology. Clinical manifestations range from mild symptom...
متن کامل[Budd Chiari syndrome].
Primary Budd-Chiari syndrome is related to thrombosis of hepatic veins or the terminal portion of the inferior vena cava. This rare disease is usually caused by multiple concurrent factors, including acquired and inherited thrombophilias. Half of the patients with primary Budd-Chiari syndrome are affected with a myeloproliferative disease, the recognition of which is largely based on the assess...
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ژورنال
عنوان ژورنال: Turkish Journal of Hematology
سال: 2020
ISSN: 1300-7777
DOI: 10.4274/tjh.galenos.2020.2019.0186